Objectives: Ectrodactyly-ectodermal dysplasia-clefting syndrome (EEC) is a rare syndrome with features of ectrodactyly, ectodermal dysplasia and cleft lip/palate. This study presents an Iranian case with classic features and oral complications.Case: We report a 20-year old female with all manifestations of this syndrome. The simultaneous presence of these three malformations is extremely rare; the incidence is estimated to be 1.5 per 100.000.000 births.Conclusion: Oral hygiene management of patients with EEC syndrome is important and dental practitioners need to know the oral and dental conditions presenting with this syndrome.

Background and aim: Ectodermal dysplasia is a hereditary disorder of ectoderm that involves teeth, skin, and hair, nails, salivary, lacrimal and sweat glands. The most common type of diseaseishypohydrotic ectodermal dysplasia that is inherited as recessive x-linked trait.The main clinical symptoms are dry skin, sparse thin hair, small brittle nails, hyperkeratosis of palms and soles, complete or partial missing of sweat glands, hypodontia and oligodontia.Case report: The patient was a six years old female with hypohydrotic ectodermal dysplasia with the chief complaint of difficult eating. The clinical and radiographic examinations showed conical teeth and microdontia, hypodontia, increased overbite, and atrophic alveolar ridge. The oral rehabilitation was performed by constructing overdentures on both jaws. The oral functions including mastication, speaking and esthetics were improved to a large extent.

Purpose: Two cases of ectodermal dysplasia with ocular manifestations are presented.Case presentation and results: The first case was a young girl with mild ocular involvement presented as dry eye and blepharitis. The second case was a 30 year-old man who presented as right corneal perforation due to severe dry eye. Dry eye in the first case was controlled with lubricants, along with treatment of blepharitis and finally punctual occlusion. Tectonic corneal graft with lateral blepharorrhaphy was performed in the second case.Conclusion: Ocular involvement in ectodermal dysplasia can present inself in a wide form. Appropriate treatment, control of dry eye blepharitis, especially in severe cases can improve ocular surface condition and preserve the eye.

Introduction: Ectodermal dysplasia is a genetic rare disease, consisting of a group of abnormalities which are the results of the abnormal development of two or more embryonic ectoderm derivatives, such as the skin, hair, nail, sweat gland, tooth, and other organs. Systemic features of ectodermal dysplasia include sparse hair (hypotrichosis), dry and hypopigmented skin, and malfunction of sweat glands that could cause hyperthermia. Intraoral symptoms of ectodermal dysplasia are abnormalities in tooth number (hypodontia or oligodontia of primary and permanent dentitions) and morphology (conical or peg tooth). Reestablishment of dental esthetics in a growing child with ectodermal dysplasia is crucial to amend psychosocial, esthetic, and functional problems. In this case report, an 8-year-old boy with esthetic and functional complaints was treated by a multidisciplinary approach. His parents declared no systemic diseases. Chief compliant of the patient was the problem in the eruption of the anterior teeth and dental abcess. The patient was reported to have major problems in terms of esthetics and social communications because of the missing teeth. The aim of this case report was to display a simple and cost-benefit method to reproduce an agreeable smile in an 8-year-old male patient with hypohidrotic ectodermal dysplasia. After the dental management in this case, the esthetics, phonetics, and chewing functions were rectified significantly. In addition, the parents reported an increased level of self-esteem in their child.

Background and aim: Ectodermal dysplasia (ED) is a hereditary disease that affects ectodermal tissues. Its oral manifestations include hypodontia or oligodontia, which cause the reduction of the height and width of the alveolar ridge. Considering numerous difficulties that these patients encounter with regard to facial appearance, talking, and chewing, their rehabilitation has a major influence on their quality of life. Implantation therapy is considered as a successful therapeutic protocol for substitution of such teeth. This article is a review of implant rehabilitation of ED patients and the related management procedures. Materials and methods: In the present review article, the English articles in PubMed, ScienceDirect, MEDLINE, and Google Scholar databases from January 2000 to December 2017 have been investigated using the following keywords: anodontia, dental implants, ectodermal dysplasia, and hypodontia. Conclusion: There is a multilateral approach to the treatment of ED patients according to their age, the status of oral soft and hard tissues and the remaining teeth. Implantation therapy for such patients is similar to that of non-ED patients.

Ectodermal dysplasia is an inherited disorder with partial or complete anodontia. Early dental treatments are mandatory for improving child mastication, communication, and esthetic. There are various treatment approaches such as implant-retained prosthesis, fixed and removable denture which should be selected according to remained teeth, oral and facial parameters. This clinical study describes the prosthetic treatment of a child with ectodermal dysplasia with combination of complete overdenture and partial removable denture.